- Case Report
- A Case of Epidermolysis Bullosa Dystrophica.
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Soon Yol Hwang, Jeong Sil Han, Gu Seok Jung, Sung Won Kim, Kil Hyun Kim, Chung Hee Chi
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Clin Exp Pediatr. 1987;30(9):1049-1054. Published online September 30, 1987
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Epidermolysis bullosa dystrophica (EBD) is a rare, chronic noninflammatory mechanobullous
disease of hereditary trait, which easily produces bulla by minor injury or spontaneously.
We experienced a case of EBD in a 27th day of life female patient. Diagnosis was confirmed by
clinical features, light and electron microscopy. A brief review of related literature was made.
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- A Case of Letterer-Siwe Disease.
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Suh Hong Ha, Jeong Sil Han, Sung Won Kim, Kyung Tae Kim, Kil Hyun Kim, Chung Hee Chi
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Clin Exp Pediatr. 1987;30(3):335-341. Published online March 31, 1987
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Letterer-Siwe disease is a variant of Histiocytosis X and characterized by onset in infancy,
hepatosplenomegaly, lymphadenopathy, bleeding tendency, hypochromic anemia, fever, localized
bone defect and fatal outcome. The diagnosis was confirmed by clinical symptoms, laboratory datas,
histopathologic and radiologic findings.
We experienced a case which was treated by single prednisolone method and resulted to good
response.
A brief review of literature was made.
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